Londoner's LIfe 20 – By Phil Ryan

Ah the London January sales! This year they have an added importance in that according to figures they may be the last big spend before austerity 2012 is completely with us all and we have to start rooting through bins courtesy of George Osborne and his millionaire pals. However getting Londoners to give up conspicuous shopping is akin to getting fish to give up water so don’t hold your breath on the collapse of the high streets just yet. So after re-adjusting to the fact that the great vague days were finally over and I could leave the twilight zone days of Christmas behind me I headed into Town. My local Council have opted for the most pathetic decorations this year – basically about ten bare bulbs and some decaying green glitter from last year blu tacked to it – giving the entire high street the appearance of a walk in STD clinic with slightly less cheer. As usual for the holiday period I had lost track of which day it actually was – constantly checking my blackberry for re-assurance. Not that which day it was mattered technically. Everything shuts or opens incomprehensibly in London at this festive time especially our superb Transport network (this year I think they were trying a ‘use your legs replacement service’ approach). The surprise strikes from the unions seem eminently reasonable as they always are at this time EVERY SINGLE year without fail. Struggling by on a £40,000 plus salary with free travel must be a drag. And I do see that working on a day you don’t fancy is a bit of a pain. But didn’t they sign up for it when they started or are their working days a pick and mix job for them? Sweet huh? Usually I support unions but this lot are now officially beyond a greedy joke. Not I might add that I have any warm feelings to the bozos that allegedly run TFL (including I might add a lot of them on hundreds of thousands of pounds to run a lousy and uncoordinated service) That all said after just twenty three handy and in no way inconvenient changes by way of Cardiff I found myself at Bond Street tube.

A friend had invited me to meet for tea and somehow just to kill some time I found myself wandering through some shops on my way there. In a sale! Oh my god. House of Fraser looked like a scene from a Bosch painting. Grim faced loons squashed together like battery chickens rummaging through masses of ugly jumpers and shirts that are only in fashion during a total eclipse. Lines of ever grimly smiling staff carefully re-folding everything a matter of minutes later. The only thing missing were bare buttocked devils gouting fire from their eyes although I think I saw a few queuing up at the Calvin Klein concession. Still in shock I made the terrible decision to pop into HMV in Oxford Street where the staff had dropped all pretence at being anything but hacked off. Two wardrobes in shirts saying security kept bellowing “Don’t block the aisles it’s a safety hazard MOVE PLEASE MOVE it’s all about SAFETY” and glaringly waving their walkie talkies around like surrogate light sabres. The counters were manned by gimlet eyed dudes who at least seemed quite chilled when they took your money although they did all have a glassy rohipnol look about them. I suspect they’d been given something. But my favourites were the harassed looking shelf re-stockers. No sooner had they ripped open a box of whatever the manic punters gathered behind them were after they would hiss loudly “Please wait until we have put them onto the shelves” presumably muttering the words “you ravenous mindless scum” under their breath judging by their pained expressions. I saw a crowd six deep virtually slobbering as for some odd reason they waited patiently behind a makeshift nylon tape barrier as some Harry Potter boxed sets of DVD’s appeared. There was a surge for goodness sake. A surge. Some grinning HMV manager kept shouting only a few left. Which quite frankly just fanned the flames. But it clearly gave him a thrill. One punter was actually holding a wand and he looked to be about thirty four.

Making my escape I finally ended up in Selfridges which I think now holds the outright London award for amazingly surreal prices and stock next to Harrods. I looked at a tie which had been slashed from £300 to just £200. And then I ran my fingers over some shirts which would’ve made Stevie Wonder gag. Honestly, bright just doesn’t come close to describing their lime electric silk and leather splendour. But just who is wearing this mad stuff and where? Especially the latest in sartorial elegance the Swarofski crystal encrusted training shoes a snip at £700.00 a pair. They finally broke my wafer thin desire to stay and fight through hordes of slow moving crowds all in thrall to the great shop. Trying to make my way down the street was like taking part in some alternate universe flash mob comedy penguin shuffle. So I left. By taxi. Heading for Patisserie Valerie and some sanity. And as per usual I noted that everything I eventually bought wasn’t in the sale. Ho hum. But do Londoner’s feel the sales are a rip off. Probably. Would Londoners like all the visitors to the sales to naff off? Definitely. But do they worry themselves about such issues? No. It’s a London thing.

No.3 London Dry Gin Review

This gin is beautifully packaged and designed in every way. I especially love the key on the bottle. This No.3 London Dry Gin from Berry Brothers & Rudd, Britain’s oldest wine and spirit merchants, uses just 3 fruits and 3 spices (the ‘botanicals’ which flavour every gin), The No.3 also comes from Berry Brothers’ home; No.3 St. James’s Street.

This is now my favourite gin. Careful though, it’s 46% ABV. It’s crisp and fresh. I also made a Gin & Tonic with it which tasted perfect. It is pure class all the way. 46% is also the perfect strength for a Dry Martini.

To make a G & T

50ml of No.3 London Dry Gin, pour into high top glass over ice, add a slice of Lemon and stir, then top up with tonic water to taste.

Dr. David Clutton is the only person to have a PhD in gin flavour, the team deliberately set out to make No.3 taste ‘as gin should’ – without the use of an excessive amount of ingredients and distilled in traditional copper pot stills without any over-elaboration. So, with classic simplicity the goal, the experts placed a robust helping of juniper – the key ingredient in any gin – at the heart of No.3. This striking juniper quality was then cleverly complemented by just 5 other fruits and spices; namely, sweet Spanish orange peel, grapefruit peel, Angelica root, Moroccan coriander and cardamom seeds.

From Waitrose RRP of £33.65 for a 70cl bottle, but it’s worth it!

www.no3gin.com or Twitter @No3Gin. 

The Kraken Black Spiced Rum Review.

The name of this rum brings out legends of the sea. The Kraken was a sea beast of myth and legend, a connotation that suits this strong, rich and black rum. Even the bottle is a reminder of the beast, the two glass handles mimic the eyes of the Kraken.

This Spiced Caribbean Rum has a thick caramel taste, it’s a wonderfully spiced liquor which goes brilliantly with coke (Krakencoke), or in a cocktail like a Perfect Storm: The Kraken poured over ice, topped with ginger beer and accompanied with a squeezed slice of lime.

 

The Kraken is 40%. It is distilled in Trinidad & Tobago from sweet molasses. It is then mixed with 14 spices including cinnamon, ginger and clove. It takes effort and time to make, and you can tell. It’s delicious.

It is a good, strong rum. I have only drank rum once before but this has changed my mind. Next time I’m out I’m having spiced rum. Everything about The Kraken is great, from the bottle, to the ad campaign, to the wonderful taste. It taste’s great neat for those who can take it, but I’ll be having it in cocktails, a lot.

 

RRP £22.99 for a 70cl bottle available mostly everywhere and online at thedrinkshop.co.uk

 

 

Montezuma's Real Chocolate Club Review

Gourmet chocolate by post, every woman’s dream? I think so. Montezuma’s chocolate club is from an innovative British firm. These handmade chocolates are absolutely divine. They are one of the best things I have ever had come through my letterbox. Perfect for those January blues.

This month the chocolates were dessert themed. They came in three sections, and each section had a bar of chocolate and truffles on top. They were: Dark Chocolate Lemon Meringue Truffles and Milk chocolate with salted peanuts and butterscotch bar, Dark chocolate Eton Mess Truffles and milk chocolate treacle tart bar and milk chocolate apple crumble truffles & Dark chocolate with orange and hazelnuts bar. It’s hard to choose a favourite as they were all as delicious as they were original. The Eton Mess and Lemon Meringue were particularly amazing.

Chocolate by post must be the greatest invention ever.

It cost £19.99pcm for a whopping 600g of hand made gourmet chocolate, including postage. You can have sign up for as long or as little as you want, or give the chocolate as a gift. Though, really, do you like anyone that much?

Lady Gaga Tops Good Celebrities List.

Lady Gaga Tops DoSomething.org’s ‘Top 20 Celebs Gone Good’ List; Sophia Bush Named ‘Fan Favorite’, Bieber Shoots up the Rankings this Year; New Trend is Couples

DoSomething.org, one of the largest U.S. organizations that helps teens take action on causes they care about, it released its fourth annual ‘Top 20 Celebs Gone Good’ list.

Lady Gaga continues her reign as the star who uses her celebrity to do the most good. Known for her support of gay rights, AIDS, and poverty, she focused primarily this year on bullying, even taking her thoughts to the White House in December. She also announced the creation of her own charity, the Born this Way Foundation, which aims to empower youth and lead them to a brave new society where each individual is accepted and loved as the person they were born to be.

Making a meteoric rise to number two this year is Justin Bieber , up from number 10 last year. His fast rise is due to his prolific work with Pencils of Promise, an organization that builds schools in Laos and Guatemala. Justin is also a consistent supporter of Make-A-Wish, raised funds for charity with his fragrance and holiday album, and recently distributed $100,000 to Whitney Elementary School in Las Vegas.

“There are some interesting trends from this year’s list,” says Aria Finger, COO of DoSomething.org. “It’s dominated by young celebrities and we also see so many couples. Last year the list had its first power couple, Ashton and Demi who have now broken up, and this year there are a total of four couples. Doing good is definitely fun in groups.”

For the first time ever, DoSomething.org’s panel of social media and mobile experts incorporated Facebook voting to help them determine the impact of celebrities reaching an audience with their cause. The criteria stipulated giving money wasn’t enough to count as creating impact; instead, a celebrity needed to take an action others could emulate, like writing articles, building houses, or founding an organization. Facebook fans voted Sophia Bush as the first ‘Fan Favorite.’

The 2011 ‘Top 20 Celebs Gone Good’ list:

1. Lady Gaga
2. Justin Bieber
3. George Clooney
4. Will & Jada Pinkett Smith
5. Leonardo DiCaprio
6. Matt Damon
7. Ellen DeGeneres
8. Brad Pitt & Angelina Jolie
9. Dwight Howard
10. Demi Lovato
11. Shakira
12. Ashton Kutcher & Demi Moore
13. will.i.am
14. Blake Shelton & Miranda Lambert
15. Nick Cannon
16. Lea Michele
17. Daniel Radcliffe
18. Miley Cyrus
19. Coldplay
20. Taylor Swift

“There are a handful of other celebrities who just missed the cut-off this year,” notes Finger. “We look forward to seeing what they will do in 2012.” Current speculations and predictions from DoSomething.org include:

* Will Jay-Z and Beyonce, Rihanna, and Justin Timberlake each use their massive popularity and talent for social change next year?
* How will Zoey Dechanel use her new star power for good?
* We suspect Bieber’s good heart will rub-off on Selena Gomez and catapult her to the list next year.
* With Tim Tebow being the most talked about athlete of 2011, we’re excited to see how he uses his celebrity for good in the coming year.

To determine the rankings, DoSomething.org used its research team and an expert panel, who focused on three elements: popularity, influence, and impact. The first two were calculated using each celebrity’s number of Twitter followers and Facebook likes, as well as their IMDB Pro Scores, Billboard Social 50 ranking, and number of ChaCha inquiries.

For full list and celebrities’ individual charitable impact, visit: Celebrities doing good.

BOARDWALK EMPIRE SEASON 2

American cable network HBO’s modus operandi seems reliably similar across many of its shows. A large array of characters interacting on an arresting, gigantic backdrop and slowly building up their story arcs with one another before tying them together in a steadily escalating rush to the end. Those seeking immediate, self contained thrills each and every week should look toward FOX and ABC for such shows. This approach extends to HBO’s current hot ticket Boardwalk Empire; an epic, lavish and violent show set in Atlantic City at the beginning of prohibition in the 1920’s and the explosion of organised crime that followed. Central to the action is Enoch ‘Nucky’ Thompson (played by American indie king Steve Buscemi), the county treasurer with an eye for opportunity and loose morals. He straddles the worlds of both law and crime effortlessly ensuring that he, his corrupt sheriff brother Eli (Shea Whigham) and their cronies come out of a situation with their wallets bursting. As the drama unfolds Nucky contends with both infamous historical figures of the time; Arnold Rothstein (Michael Sthulbarg) and Al Capone (Stephen Graham), and with fictional counterparts such as unhinged war veteran/prodigy Jimmy Darmody (Michael Pitt), widow turned mistress Margaret Schroder (Kelly MacDonald) and zealous Federal Agent Nelson Van Alden (Michael Shannon).

Due to the delayed release of season one in the UK, we had the pleasure of both seasons only being separated by a few months. At the outset of season two Nucky and Margaret are living together seemingly contented. Yet this is shattered when Eli and Jimmy, the latter spurned on by his domineering mother Gillian (Gretchen Moll), lead an open rebellion against Nucky’s leadership with the alcohol flowing into the city proving the key factor. Battle lines are drawn, blood ties are broken and bodies drop like flies as both sides struggle to hold onto what both believe are theirs.

The most easily recognizable aspect of Boardwalk Empire’s quality is its look and design. Every scene, every location and arguably every frame are immaculate to a tee and the cinematography and visual effects weigh up just as much. The show is produced by master filmmaker Martin Scorsese (who also directed the pilot episode) and his influence and sway clearly show and not just in the visual department. As a whole the show engages with the love/hate relationship between America and the almost mythic figure of the organised criminal. There is nothing as trivial as good and bad in this world; the viewer has to use their own moral compass to determine who is the least evil. The theme of betrayal and mistrust runs throughout this season as protégé’s turn against mentors and families against their own. This comes to a head particularly in the penultimate episode where we discover the cause of the friction between Jimmy and Gillian as their story takes a turn similar to Oedipus Rex. The tension is practically unbearable as…well let’s just say things get Freudian. Very Freudian…

The performances of Boardwalk Empire are frequently cited as its major draw. Indeed any show with Steve Buscemi at the helm is worthy of all attention. As well as playing to the strengths of confidence and arrogance that have permeated through many of the characters he has played in the past, there is a vulnerability to Nucky that allows Buscemi to tap into emotional depths that perhaps he has not had the chance to truly reach in previous roles. His roles opposite his brother, from both fisticuffs to graveside revelations, are nothing short of heart-breaking. Michael Pitt proves an almost perfect foil, his youthful charm and handsomeness are a sidestep diversion to Jimmy’s brutality and crumbling psyche under the pressure of demon parents and gangster dealings. His eyes are deep and expressive but there is an underlying darkness that is sometimes genuinely terrifying. Pitt has utilised similar skills on the independent circuit and it’s a pleasure to see them demonstrated on a mainstream outlet. There are equally impressive turns amongst the supporting cast, most underrated amongst them being perhaps British actor Jack Huston as disfigured veteran turned hitman Richard Harrow, a role that despite being delivered beneath a prosthetic mask rings with tortured emotion.

Unfortunately it is in the initial portrayal of its female characters that the show falls down. Model turned actress Paz de la Huerta is saddled with an inconsequential role as Nucky’s former mistress Lucy, a role that could have more impact if it were not for de la Huerta’s inert performance; every line reading is as flat as the Ferns’. Her poor performance would be less distracting if the shows maker didn’t insist on her being nude in the majority of her scenes. Aleksa Palladino fares a little better as Jimmy’s unsatisfied artist wife Angela. Her performance is fine yet she is given little material to work with which makes a particular end of game plot revelation lack the gut punch it deserves. Thankfully there are two roles for women in the show that stand tall and proud; Kelly MacDonald and Gretchen Moll. When we meet Margaret Schroder in season one she appears initially as an oppressed victim who slowly but steadily reacts with confidence and assuredness to her changing circumstances. Ranging from deceiving lawman to fending off attackers via shotgun, MacDonald is a tour de force of vulnerability and uncertainty; her later scenes as she grapples with her personal guilt never lapse over into sentimentality. On the flip side of this Gretchen Moll inhabits the role of Gillian with such chilling venom (‘You will not be disrespected!’) with moments of breathtaking clarity into her characters inner torment. An early scene where she confronts the invalid man who violated her as a child is perfectly paced; drawing in with allusion, steady reveal and a final devastating explosion in violence. A sympathetic villain if there ever was one.
All in all Boardwalk Empire has played like crafty card shark. It knows exactly when to show its big hand yet also feels like its holding a lot of tension back. Every jaw dropping set piece or character moments is bookended by copious amounts of exposition and the sense of characters moving into place though on a large chess board. It is these moments of sheer muscular strength that make the show a force to be reckoned with and earn the patience during its quieter moments. It has been renewed for a third season and after its powerful final seasons there is the strong hope that these two first seasons have laid the groundwork for the true fireworks. Even still below par HBO is miles ahead of the competition and with Buscemi and MacDonald at the helm, anything is possible.

Boardwalk Empire Season 2 finale was broadcast on Christmas Eve. Boardwalk Empire – Season 1 (HBO) [DVD]

Londoners Life 19 – By Phil Ryan

Londoners Life 19 – By Phil Ryan

Well a big hello after my absence. Had to finish off two novels and some other projects. But I’m back in time for my New Year review. London has had a busy old time in many ways. We’ve watched the giant money hole of the Olympics steal more and more of our money, we’ve had a bit of rioting, a bit of demonstrating and a bit of a recession. And how’s it left us Londoners? Well certainly the gap between rich and poor continues apace – some areas in London now resembling scenes from the aftermath of an apocalyptic plague movie whilst other tangibly smell of cash and cashmere. This gap can also be measured in ever sky rocketing house prices. Whilst everyday living costs creep ever higher. So for my review of 2011 here’s a quick list of a few London change indicators.
• Starters in restaurants now seem to cost as much as a main course
• More restaurants have replaced their chairs with those highly comfortable solid wooden thin benches from a Victorian prison
• A trip to the cinema for two is coming in at close to £25.00 and popcorn has broken the £5.00 ceiling
• There’s a new demonstration every day in Town not to mention various permanent demonstrations at tourist sights
• The Oyster card now only offers minor convenience in getting in and out of stations but cleverly hides the ever spiraling travel costs (until you have to top up)
• Parking in London is now only affordable by the wealthy or the desperate
• London Councils have finally abandoned all pretense of caring about their residents.
• Shops have sales every other week
• Sushi restaurants are taking over
So goodbye to 2011 with your momentous world events that touched London but didn’t fundamentally alter it in any way. For keen power player watchers we’ve had scandals and phone hacking saga’s that apart from the closure of the News of the World don’t seem to have changed the main players. Our Bankers carry on as normal apart from those lower down the food chain losing their jobs. So from a Londoners perspective what’s 2012 going to be like? Well it’s going to be more expensive across the board from transport to accommodation. The Olympic gravy train will roll in and out inconveniencing us all (of course TFL will run a fantastic tube service with an extra 6 million people on board) And there’ll probably be another uplifting parade to celebrate the royal baby that will undoubtedly appear in time for the Queens Jubilee celebrations. Closer to home still Hammersmith Bridge will be finally replaced by Lego as that seems more robust than the one they spent millions of our taxes on ‘repairing’. The Mayoral election will shock us all when a surprise last minute candidate bags the top job. Said candidate being that bloke off my big fat gypsy wedding. And London Councils will begin plans to cull the poor.

Looking back I’m left with some of my favourite moments from what I can only describe as ‘spokespeople’. TV and Radio reporters grabbing that all important human interest moment out on the street. So from ‘Rioters in Tottenham’ we had (from young guy number 1 with a hoodie and face mask carrying a large plasma TV) “It’s all about Iraq” (from young man number 2 with a hoodie and face mask number) “It’s about anger. We’re angry about being angry”. From a ‘St Pauls Cathedral Camp protester’ (who looked slightly the worse for wear) “I came to support these people and whatever it is they’re protesting about – it’s brilliant whatever it is and they gave me a tent a spliff and some soup I mean how great is that?” From a Christmas shoppers laden with about ten bags “Yes we’re cutting right back this year” and from some religious loon with a beard “Threatening death for us is an argument it’s not unreasonable”. So Happy 2012 to us all and whether its Ken or Boris as Mayor, whether we win gold medals or flog the Olympic venues for a tenner to a friend of Lord Coe’s as Londoner’s we just won’t care – It’s a London thing.

Krabbe: The Disease That Needs More Awareness

I had not heard of Krabbe disease until 2011, when a relative was diagnosed with it. Krabbe is also called Globoid cell leukodystrophy; Galactosylcerebrosidase deficiency; Galactosylceramidase deficiency. It is a rare genetic disorder of the nervous system and is a type of leukodystrophy. It is named after the Danish neurologist Knud Haraldsen Krabbe who discovered it.

Krabbe disease is caused by a defect in the GALC gene. People with this gene defect don’t make enough of a substance called galactocerebroside beta-galactosidase (galactosylceramidase).

This is needed by the body to make myelin, the material that surrounds and protects nerve fibers. Myelin breaks down without it, brain cells die, and nerves in the brain and other body areas do not work properly.

There are two forms of Krabbe disease.

  • Early-onset Krabbe disease appears in the first months of life.
  • Late-onset Krabbe disease begins in late childhood or early adolescence.

Krabbe disease is inherited, which means that it runs in families. To get this disease, each of your parents must pass you a copy of the faulty GALC gene.

This condition is very rare, Affecting 1 in 100,000 births.

Symptoms

  • Changing muscle tone from floppy to rigid.
  • Hearing loss that leads to deafness
  • Feeding difficulties
  • Irritability and sensitivity to loud sounds
  • Severe seizures
  • Unexplained fevers
  • Vision loss that leads to blindness
  • Vomiting

The condition is often misdiagnosed as cerebral palsy.

There is no specific treatment for Krabbe disease.It is possible to have a bone marrow transplant in the early stages of the disease, but this treatment has risks.The outcome of Krabbe is usually not good. On average, infants with Krabbe die before age 2. People who develop the disease at a later age have survived into adulthood with nervous system disease.

A blood test can be done to see if you carry the gene for Krabbe disease and prenatal tests can be done to screen a developing baby for this condition.

http://www.savebabiesuk.org/

United Leukodystrophy Foundation — www.ulf.org

http://www.krabbes.com/

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